Health-related quality of life and its relation to disease severity in boys with Duchenne muscular dystrophy: satisfied boys, worrying parents--a case-control study
Publication year
2014Source
Journal of Child Neurology, 29, 11, (2014), pp. 1486-95ISSN
Publication type
Article / Letter to editor
Display more detailsDisplay less details
Organization
Rehabilitation
Neurology
Journal title
Journal of Child Neurology
Volume
vol. 29
Issue
iss. 11
Page start
p. 1486
Page end
p. 95
Subject
Radboudumc 3: Disorders of movement DCMN: Donders Center for Medical Neuroscience; Radboudumc 3: Disorders of movement RIHS: Radboud Institute for Health SciencesAbstract
The progression of Duchenne muscular dystrophy is expected to negatively influence the patients' health-related quality of life, but knowledge of the relationship with disease severity is limited. We investigated the relationship between health-related quality of life (KIDSCREEN-52 questionnaire) and disease severity (clinical assessments of body functions and activities) in 40 boys with Duchenne muscular dystrophy (19 ambulant, 21 wheelchair dependent) who were in different phases of the disease and underwent life-limiting events such as the loss of the ability to ambulate and the ability to lift the arms. In addition, we compared boys' health-related quality of life perceptions with that of their parents. The participants' health-related quality of life was similar to healthy peers' and not influenced by disease severity, except for the physical domain. Parents scored much lower than the boys on the KIDSCREEN-52 domains Self Perception, Moods and Emotions, and Bullying. The latter finding needs attention in the management of Duchenne muscular dystrophy.
This item appears in the following Collection(s)
- Academic publications [243984]
- Faculty of Medical Sciences [92811]
Upload full text
Use your RU credentials (u/z-number and password) to log in with SURFconext to upload a file for processing by the repository team.